AGAP9

Chr 10

ArfGAP with GTPase domain, ankyrin repeat and PH domain 9

Also known as: AGAP-9, CTGLF6, bA301J7.2

The AGAP9 protein functions as a GTPase-activating protein that regulates GTPase activity. Mutations in AGAP9 cause autosomal recessive intellectual disability with developmental delay. The inheritance pattern is autosomal recessive.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
49
P/LP submissions
P/LP missense
LOEUF
DN
Mechanism· predicted
Clinical SummaryAGAP9
📋
ClinVar Variants
49 unique Pathogenic / Likely Pathogenic· 20 VUS of 113 total submissions

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.78top 25%
GOF
0.6051th %ile
LOF
0.3746th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

113 submitted variants in ClinVar

Classification Summary

Pathogenic33
Likely Pathogenic16
VUS20
Likely Benign4
Benign39
33
Pathogenic
16
Likely Pathogenic
20
VUS
4
Likely Benign
39
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
33
Likely Pathogenic
16
VUS
20
Likely Benign
4
Benign
39
Total112

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

AGAP9 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
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