ADNP2

Chr 18

ADNP homeobox 2

Also known as: ZNF508

ADNP2 encodes a DNA-binding transcription factor that regulates gene expression and is predicted to be involved in nervous system development. Mutations cause neurodevelopmental disorders with intellectual disability, typically presenting in early childhood. The gene follows autosomal dominant inheritance and shows high constraint against loss-of-function variants (LOEUF 0.39), indicating that such variants are likely pathogenic.

Summary from RefSeq, UniProt
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0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.39
LOEUF
LOF
Mechanism· predicted
Clinical SummaryADNP2
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.70) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.39LOEUF
pLI 0.696
Z-score 4.08
OE 0.20 (0.110.39)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.34Z-score
OE missense 0.96 (0.901.03)
596 obs / 619.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.110.39)
00.351.4
Missense OE0.96 (0.901.03)
00.61.4
Synonymous OE1.17
01.21.6
LoF obs/exp: 6 / 30.2Missense obs/exp: 596 / 619.8Syn Z: -2.14
DN
0.3097th %ile
GOF
0.2099th %ile
LOF
0.71top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.39

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ADNP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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