ACBD6

Chr 1AR

acyl-CoA binding domain containing 6

Also known as: NEDPM

The ACBD6 protein binds long-chain acyl-coenzyme A molecules, particularly unsaturated fatty acyl-CoAs, and participates in protein N-myristoylation. Biallelic mutations cause autosomal recessive neurodevelopmental disorder with progressive movement abnormalities. The gene shows relatively low constraint against loss-of-function variants (pLI 0.000002, LOEUF 1.129).

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.131 OMIM phenotype
Clinical SummaryACBD6
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
💊
Clinical Trials
1 active or recruiting trial — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.13LOEUF
pLI 0.000
Z-score 1.18
OE 0.68 (0.431.13)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.11Z-score
OE missense 0.98 (0.851.12)
144 obs / 147.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.68 (0.431.13)
00.351.4
Missense OE0.98 (0.851.12)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 11 / 16.1Missense obs/exp: 144 / 147.7Syn Z: -0.44

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ACBD6 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
Open Research Assistant →