ACAP2

Chr 3

ArfGAP with coiled-coil, ankyrin repeat and PH domains 2

Also known as: CENTB2, CNT-B2

Enables GTPase activator activity. Acts upstream of or within actin filament-based process. Located in ruffle. [provided by Alliance of Genome Resources, Apr 2025]

OMIMResearchGenerating clinical summary…
LOEUF 0.32
Clinical SummaryACAP2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.92). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
45 VUS of 72 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint?
0.32LOEUF
pLI 0.923
Z-score 5.42
OE 0.19 (0.120.32)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint?
3.22Z-score
OE missense 0.55 (0.490.61)
224 obs / 406.7 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios?
LoF OE?0.19 (0.120.32)
00.351.4
Missense OE?0.55 (0.490.61)
00.61.4
Synonymous OE?0.84
01.21.6
LoF obs/exp: 10 / 52.3Missense obs/exp: 224 / 406.7Syn Z: 1.55

ClinVar Variant Classifications

72 submitted variants in ClinVar

Classification Summary

VUS45
Likely Benign1
45
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
0
0
0
Likely Pathogenic
0
0
0
0
0
VUS
0
45
0
0
45
Likely Benign
0
0
0
1
1
Benign
0
0
0
0
0
Total0450146

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

38 pathogenic / likely-pathogenic (of 50) ClinVar copy-number / structural variants overlap ACAP2 — these span large chromosomal regions, not the gene specifically, and are excluded from the counts above. Explore in CNV tools →

Protein Context — Lollipop Plot

ACAP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →