ABCE1

Chr 4

ATP binding cassette subfamily E member 1

Also known as: ABC38, OABP, RLI, RLI1, RNASEL1, RNASELI, RNS4I

The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the OABP subfamily. Alternatively referred to as the RNase L inhibitor, this protein functions to block the activity of ribonuclease L. Activation of ribonuclease L leads to inhibition of protein synthesis in the 2-5A/RNase L system, the central pathway for viral interferon action. Two transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008]

OMIMResearchGenerating clinical summary…

Clinical highlights

Interpreting a novel variant
This gene is strongly intolerant of loss-of-function variation in the population, so LoF variants warrant close attention. No curated mechanism annotation is available — see the mechanism card for the computational prediction and its caveats.Based on population constraint only.
0
Active trials
24
Pubs (1 yr)
P/LP submissions
P/LP missense
0.31
LOEUF· LoF intol.
LOF
Mechanism· predicted

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint?
0.31LOEUF
pLI 0.974
Z-score 4.78
OE 0.16 (0.090.31)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint?
4.10Z-score
OE missense 0.35 (0.300.41)
112 obs / 317.7 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios?
LoF OE?0.16 (0.090.31)
00.351.4
Missense OE?0.35 (0.300.41)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 6 / 37.7Missense obs/exp: 112 / 317.7Syn Z: 0.93

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ABCE1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →