ABCC2

Chr 10

ATP binding cassette subfamily C member 2

Also known as: ABC30, CMOAT, DJS, MRP2, cMRP

The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the MRP subfamily which is involved in multi-drug resistance. This protein is expressed in the canalicular (apical) part of the hepatocyte and functions in biliary transport. Substrates include anticancer drugs such as vinblastine; therefore, this protein appears to contribute to drug resistance in mammalian cells. Several different mutations in this gene have been observed in patients with Dubin-Johnson syndrome (DJS), an autosomal recessive disorder characterized by conjugated hyperbilirubinemia. [provided by RefSeq, Jul 2008]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtDubin-Johnson syndrome
1
Active trials
161
Pubs (1 yr)
P/LP submissions
P/LP missense
1.16
LOEUF
Multiple*
Mechanism· predicted
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GeneReview available — ABCC2
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.16LOEUF
pLI 0.000
Z-score 0.38
OE 0.95 (0.791.16)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.99Z-score
OE missense 1.10 (1.041.16)
863 obs / 784.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.95 (0.791.16)
00.351.4
Missense OE?1.10 (1.041.16)
00.61.4
Synonymous OE?1.03
01.21.6
LoF obs/exp: 73 / 76.6Missense obs/exp: 863 / 784.6Syn Z: -0.41

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ABCC2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.