A4GALT

Chr 22

alpha 1,4-galactosyltransferase (P1PK blood group)

Also known as: A14GALT, A4GALT1, Gb3S, P(k), P1, P1PK, PK

The protein encoded by this gene catalyzes the transfer of galactose to lactosylceramide to form globotriaosylceramide, which has been identified as the P(k) antigen of the P blood group system. This protein, a type II membrane protein found in the Golgi, is also required for the synthesis of the bacterial verotoxins receptor. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Dec 2015]

ResearchGenerating clinical summary…

Clinical highlights

Gene-disease validity (ClinGen)
A4GALT-congenital disorder of glycosylation · ARDefinitivesufficient evidence for diagnostic panels
0
Active trials
15
Pubs (1 yr)
P/LP submissions
P/LP missense
1.65
LOEUF
Mechanism
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.65LOEUF
pLI 0.000
Z-score 0.15
OE 0.95 (0.551.65)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.19Z-score
OE missense 1.03 (0.931.15)
241 obs / 233.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.95 (0.551.65)
00.351.4
Missense OE?1.03 (0.931.15)
00.61.4
Synonymous OE?1.12
01.21.6
LoF obs/exp: 8 / 8.5Missense obs/exp: 241 / 233.0Syn Z: -0.99

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

A4GALT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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