FAM9A

Chr X

family with sequence similarity 9 member A

The encoded protein is a nuclear protein localized to the nucleolus with similarity to synaptonemal complex proteins. This X-linked gene shows very low constraint against loss-of-function variants, and currently no specific disease associations have been established in the provided data. The gene arose through duplication events on the X chromosome and would follow X-linked inheritance patterns.

OMIMResearchSummary from RefSeq
GOFmechanismLOEUF 1.91
Clinical SummaryFAM9A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.91LOEUF
pLI 0.000
Z-score -1.29
OE 1.43 (0.941.91)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.75Z-score
OE missense 1.19 (1.041.37)
145 obs / 121.7 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.43 (0.941.91)
00.351.4
Missense OE1.19 (1.041.37)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 15 / 10.5Missense obs/exp: 145 / 121.7Syn Z: -0.29

This gene — mechanism propensity

DN
0.6163th %ile
GOF
0.77top 25%
LOF
0.2386th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FAM9A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found